Effect of elexacaftor–tezacaftor–ivacaftor on bronchial dilatations in adolescents with cystic fibrosis: a multicentre prospective observational study

Isabelle Sermet-Gaudelus, Alexia Letierce, Laureline Berteloot, Anne-Sophie Bonnel, Yuxin Chen, Punit Makani, Mairead Kelly-Aubert, Feriel Kanoun, Lucille Penalva, Nesrine Bouleghem, Tiphaine Bihouee, Stéphanie Bui, Harriet Corvol, Véronique Houdouin, Marie Mittaine, Aurelie Tatopoulos, Laurence Weiss, Nathalie Wizla, Nathalie Kapel, Antoine Bessou, H A W M Tiddens, Daan Caudri, Philippe Reix, Christophe Marguet, Marianne Alison, Baptiste Arnouat, Melissande Baravalle, Mahassen Barboura, Jeanne Barillon, Audrey Barzic, Lilia Benhalla, Myriam Benhamida, Khadidja Bennour, Katia Bessaci, Antoine Bessou, Marie Biard, Aurore Blonde, Bertrand Bruneau, Aline Carsin-Vu, Mathilde Casson-Masselin, Frédérique Chedevergne, Camille Cisterne, Laure Cosson, Laure Couderc, Carole Couette, Marie-Laure Dalphin, Paola de Carli, Eric Deneuville, Gael Dournes, Valerie Douzal, Hubert Ducou-le-Pointe, Clemence Dufour-Barba, Raphael Enaud, Mathilde Ferry, Morgane Floch, Pierre Foucaud, Flaviu Gabor, Asma Gabsi, Elsa Gachelin, Charlotte Giraud, Fatiha Hassani, Audrey Herzog, Antoine Delval, Anne Houzel, Frédéric Huet, Antoine Hutt, Ahmed Kheniche, Marie Jamin, Kadiatou Kaba, Sébastien Kiefer, Guillaume Labbe, Alice Ladaurade, Jeanne Languepin, Muriel Laurans, Laurence Leclainche-Viala, Faustine Lefebvre, Thomas Lefrancois, Servane Lelez-Soquet, Marion Lenoir, Louis-Marie Lieber, Clotilde Livrozet, Catthy Llerena, Alexia Letierce, Damien Mandry, Sarah Marchal, Christophe Marguet, Sophie Mayer, Stéphane Mazur, Laurent Mely, Rania Messaoudi, Baptiste Morel, Camille Ohlmann, Jocelyne Pengam, Stéphanie Perrez, Caroline Perisson, Thomas Perrin, Isabelle Petit, Philippe Petit, Juliette Pezron, Carole Piccini-Bailly, Delphine Pouradier, Cinthia Rames, Adelaide Rega, Philippe Reix, Martine Remy, Natacha Remus, Marine Revillion, Lea Roditis, Anna R Ronayette, Flavie Sadone, Djouher Sahki, Floriane Sauvage, Manuela Scalbert, Consuelo Sebastiasancho, Isabelle Sermet-Gaudelus, Chiara Sielo, Sophie Simon, Anaelle Simonneau, Florence Socchi, Nathalie Stremler, Aurélie Tatopoulos, Matthieu Thimmesch, Diane Thomassonabdel-Latif, Guillaume Thouvenin, Caroline Thumerelle, Célia Thilliard, Jean-Yves Travers, Françoise Troussier, Sophie Vallois, Saskia Vandeperre, Julie Vial, Philippe Vigneron, Marie-Christine Werck-Gallois

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DOI: 10.1016/s2213-2600(25)00248-6
Published: 2026-01
Container: The Lancet Respiratory Medicine
Publisher: Elsevier BV
Open access: unknown

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BibTeX

@article{allodium:10.1016/s2213-2600-25-00248-6,
  title = {Effect of elexacaftor–tezacaftor–ivacaftor on bronchial dilatations in adolescents with cystic fibrosis: a multicentre prospective observational study},
  author = {Isabelle Sermet-Gaudelus and Alexia Letierce and Laureline Berteloot and Anne-Sophie Bonnel and Yuxin Chen and Punit Makani and Mairead Kelly-Aubert and Feriel Kanoun and Lucille Penalva and Nesrine Bouleghem and Tiphaine Bihouee and Stéphanie Bui and Harriet Corvol and Véronique Houdouin and Marie Mittaine and Aurelie Tatopoulos and Laurence Weiss and Nathalie Wizla and Nathalie Kapel and Antoine Bessou and H A W M Tiddens and Daan Caudri and Philippe Reix and Christophe Marguet and Marianne Alison and Baptiste Arnouat and Melissande Baravalle and Mahassen Barboura and Jeanne Barillon and Audrey Barzic and Lilia Benhalla and Myriam Benhamida and Khadidja Bennour and Katia Bessaci and Antoine Bessou and Marie Biard and Aurore Blonde and Bertrand Bruneau and Aline Carsin-Vu and Mathilde Casson-Masselin and Frédérique Chedevergne and Camille Cisterne and Laure Cosson and Laure Couderc and Carole Couette and Marie-Laure Dalphin and Paola de Carli and Eric Deneuville and Gael Dournes and Valerie Douzal and Hubert Ducou-le-Pointe and Clemence Dufour-Barba and Raphael Enaud and Mathilde Ferry and Morgane Floch and Pierre Foucaud and Flaviu Gabor and Asma Gabsi and Elsa Gachelin and Charlotte Giraud and Fatiha Hassani and Audrey Herzog and Antoine Delval and Anne Houzel and Frédéric Huet and Antoine Hutt and Ahmed Kheniche and Marie Jamin and Kadiatou Kaba and Sébastien Kiefer and Guillaume Labbe and Alice Ladaurade and Jeanne Languepin and Muriel Laurans and Laurence Leclainche-Viala and Faustine Lefebvre and Thomas Lefrancois and Servane Lelez-Soquet and Marion Lenoir and Louis-Marie Lieber and Clotilde Livrozet and Catthy Llerena and Alexia Letierce and Damien Mandry and Sarah Marchal and Christophe Marguet and Sophie Mayer and Stéphane Mazur and Laurent Mely and Rania Messaoudi and Baptiste Morel and Camille Ohlmann and Jocelyne Pengam and Stéphanie Perrez and Caroline Perisson and Thomas Perrin and Isabelle Petit and Philippe Petit and Juliette Pezron and Carole Piccini-Bailly and Delphine Pouradier and Cinthia Rames and Adelaide Rega and Philippe Reix and Martine Remy and Natacha Remus and Marine Revillion and Lea Roditis and Anna R Ronayette and Flavie Sadone and Djouher Sahki and Floriane Sauvage and Manuela Scalbert and Consuelo Sebastiasancho and Isabelle Sermet-Gaudelus and Chiara Sielo and Sophie Simon and Anaelle Simonneau and Florence Socchi and Nathalie Stremler and Aurélie Tatopoulos and Matthieu Thimmesch and Diane Thomassonabdel-Latif and Guillaume Thouvenin and Caroline Thumerelle and Célia Thilliard and Jean-Yves Travers and Françoise Troussier and Sophie Vallois and Saskia Vandeperre and Julie Vial and Philippe Vigneron and Marie-Christine Werck-Gallois},
  year = {2026},
  journal = {The Lancet Respiratory Medicine},
  doi = {10.1016/s2213-2600(25)00248-6},
  url = {https://doi.org/10.1016/s2213-2600(25)00248-6}
}

RIS

TY  - JOUR
TI  - Effect of elexacaftor–tezacaftor–ivacaftor on bronchial dilatations in adolescents with cystic fibrosis: a multicentre prospective observational study
AU  - Isabelle Sermet-Gaudelus
AU  - Alexia Letierce
AU  - Laureline Berteloot
AU  - Anne-Sophie Bonnel
AU  - Yuxin Chen
AU  - Punit Makani
AU  - Mairead Kelly-Aubert
AU  - Feriel Kanoun
AU  - Lucille Penalva
AU  - Nesrine Bouleghem
AU  - Tiphaine Bihouee
AU  - Stéphanie Bui
AU  - Harriet Corvol
AU  - Véronique Houdouin
AU  - Marie Mittaine
AU  - Aurelie Tatopoulos
AU  - Laurence Weiss
AU  - Nathalie Wizla
AU  - Nathalie Kapel
AU  - Antoine Bessou
AU  - H A W M Tiddens
AU  - Daan Caudri
AU  - Philippe Reix
AU  - Christophe Marguet
AU  - Marianne Alison
AU  - Baptiste Arnouat
AU  - Melissande Baravalle
AU  - Mahassen Barboura
AU  - Jeanne Barillon
AU  - Audrey Barzic
AU  - Lilia Benhalla
AU  - Myriam Benhamida
AU  - Khadidja Bennour
AU  - Katia Bessaci
AU  - Antoine Bessou
AU  - Marie Biard
AU  - Aurore Blonde
AU  - Bertrand Bruneau
AU  - Aline Carsin-Vu
AU  - Mathilde Casson-Masselin
AU  - Frédérique Chedevergne
AU  - Camille Cisterne
AU  - Laure Cosson
AU  - Laure Couderc
AU  - Carole Couette
AU  - Marie-Laure Dalphin
AU  - Paola de Carli
AU  - Eric Deneuville
AU  - Gael Dournes
AU  - Valerie Douzal
AU  - Hubert Ducou-le-Pointe
AU  - Clemence Dufour-Barba
AU  - Raphael Enaud
AU  - Mathilde Ferry
AU  - Morgane Floch
AU  - Pierre Foucaud
AU  - Flaviu Gabor
AU  - Asma Gabsi
AU  - Elsa Gachelin
AU  - Charlotte Giraud
AU  - Fatiha Hassani
AU  - Audrey Herzog
AU  - Antoine Delval
AU  - Anne Houzel
AU  - Frédéric Huet
AU  - Antoine Hutt
AU  - Ahmed Kheniche
AU  - Marie Jamin
AU  - Kadiatou Kaba
AU  - Sébastien Kiefer
AU  - Guillaume Labbe
AU  - Alice Ladaurade
AU  - Jeanne Languepin
AU  - Muriel Laurans
AU  - Laurence Leclainche-Viala
AU  - Faustine Lefebvre
AU  - Thomas Lefrancois
AU  - Servane Lelez-Soquet
AU  - Marion Lenoir
AU  - Louis-Marie Lieber
AU  - Clotilde Livrozet
AU  - Catthy Llerena
AU  - Alexia Letierce
AU  - Damien Mandry
AU  - Sarah Marchal
AU  - Christophe Marguet
AU  - Sophie Mayer
AU  - Stéphane Mazur
AU  - Laurent Mely
AU  - Rania Messaoudi
AU  - Baptiste Morel
AU  - Camille Ohlmann
AU  - Jocelyne Pengam
AU  - Stéphanie Perrez
AU  - Caroline Perisson
AU  - Thomas Perrin
AU  - Isabelle Petit
AU  - Philippe Petit
AU  - Juliette Pezron
AU  - Carole Piccini-Bailly
AU  - Delphine Pouradier
AU  - Cinthia Rames
AU  - Adelaide Rega
AU  - Philippe Reix
AU  - Martine Remy
AU  - Natacha Remus
AU  - Marine Revillion
AU  - Lea Roditis
AU  - Anna R Ronayette
AU  - Flavie Sadone
AU  - Djouher Sahki
AU  - Floriane Sauvage
AU  - Manuela Scalbert
AU  - Consuelo Sebastiasancho
AU  - Isabelle Sermet-Gaudelus
AU  - Chiara Sielo
AU  - Sophie Simon
AU  - Anaelle Simonneau
AU  - Florence Socchi
AU  - Nathalie Stremler
AU  - Aurélie Tatopoulos
AU  - Matthieu Thimmesch
AU  - Diane Thomassonabdel-Latif
AU  - Guillaume Thouvenin
AU  - Caroline Thumerelle
AU  - Célia Thilliard
AU  - Jean-Yves Travers
AU  - Françoise Troussier
AU  - Sophie Vallois
AU  - Saskia Vandeperre
AU  - Julie Vial
AU  - Philippe Vigneron
AU  - Marie-Christine Werck-Gallois
PY  - 2026
JO  - The Lancet Respiratory Medicine
DO  - 10.1016/s2213-2600(25)00248-6
UR  - https://doi.org/10.1016/s2213-2600(25)00248-6
ER  -

APA

Sermet-Gaudelus, I., Letierce, A., Berteloot, L., Bonnel, A., Chen, Y., Makani, P., Kelly-Aubert, M., Kanoun, F., Penalva, L., Bouleghem, N., Bihouee, T., Bui, S., Corvol, H., Houdouin, V., Mittaine, M., Tatopoulos, A., Weiss, L., Wizla, N., Kapel, N., Bessou, A., Tiddens, H. A. W. M., Caudri, D., Reix, P., Marguet, C., Alison, M., Arnouat, B., Baravalle, M., Barboura, M., Barillon, J., Barzic, A., Benhalla, L., Benhamida, M., Bennour, K., Bessaci, K., Bessou, A., Biard, M., Blonde, A., Bruneau, B., Carsin-Vu, A., Casson-Masselin, M., Chedevergne, F., Cisterne, C., Cosson, L., Couderc, L., Couette, C., Dalphin, M., Carli, P. D., Deneuville, E., Dournes, G., Douzal, V., Ducou-le-Pointe, H., Dufour-Barba, C., Enaud, R., Ferry, M., Floch, M., Foucaud, P., Gabor, F., Gabsi, A., Gachelin, E., Giraud, C., Hassani, F., Herzog, A., Delval, A., Houzel, A., Huet, F., Hutt, A., Kheniche, A., Jamin, M., Kaba, K., Kiefer, S., Labbe, G., Ladaurade, A., Languepin, J., Laurans, M., Leclainche-Viala, L., Lefebvre, F., Lefrancois, T., Lelez-Soquet, S., Lenoir, M., Lieber, L., Livrozet, C., Llerena, C., Letierce, A., Mandry, D., Marchal, S., Marguet, C., Mayer, S., Mazur, S., Mely, L., Messaoudi, R., Morel, B., Ohlmann, C., Pengam, J., Perrez, S., Perisson, C., Perrin, T., Petit, I., Petit, P., Pezron, J., Piccini-Bailly, C., Pouradier, D., Rames, C., Rega, A., Reix, P., Remy, M., Remus, N., Revillion, M., Roditis, L., Ronayette, A. R., Sadone, F., Sahki, D., Sauvage, F., Scalbert, M., Sebastiasancho, C., Sermet-Gaudelus, I., Sielo, C., Simon, S., Simonneau, A., Socchi, F., Stremler, N., Tatopoulos, A., Thimmesch, M., Thomassonabdel-Latif, D., Thouvenin, G., Thumerelle, C., Thilliard, C., Travers, J., Troussier, F., Vallois, S., Vandeperre, S., Vial, J., Vigneron, P., & Werck-Gallois, M. (2026). Effect of elexacaftor–tezacaftor–ivacaftor on bronchial dilatations in adolescents with cystic fibrosis: a multicentre prospective observational study. The Lancet Respiratory Medicine. https://doi.org/10.1016/s2213-2600(25)00248-6

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crossref · retrieved 2026-09-26T11:47:39.438Z