Biallelic pathogenic variants in the lanosterol synthase gene LSS involved in the cholesterol biosynthesis cause alopecia with intellectual disability, a rare recessive neuroectodermal syndrome

Thomas Besnard, Natacha Sloboda, Alice Goldenberg, Sébastien Küry, Benjamin Cogné, Flora Breheret, Eva Trochu, Solène Conrad, Marie Vincent, Wallid Deb, Xavier Balguerie, Sébastien Barbarot, Geneviève Baujat, Tawfeg Ben-Omran, Anne-Claire Bursztejn, Virginie Carmignac, Alexandre N. Datta, Aline Delignières, Laurence Faivre, Betty Gardie, Jean-Louis Guéant, Paul Kuentz, Marion Lenglet, Marie-Cécile Nassogne, Vincent Ramaekers, Rhonda E. Schnur, Yue Si, Erin Torti, Julien Thevenon, Pierre Vabres, Lionel Van Maldergem, Dorothea Wand, Arnaud Wiedemann, Bertrand Cariou, Richard Redon, Antonin Lamazière, Stéphane Bézieau, Francois Feillet, Bertrand Isidor

Open source

DOI
10.1038/s41436-019-0445-x
Published
2019-09
Container
Genetics in Medicine
Publisher
Elsevier BV
Open access
unknown

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BibTeX

@article{allodium:10.1038/s41436-019-0445-x,
  title = {Biallelic pathogenic variants in the lanosterol synthase gene LSS involved in the cholesterol biosynthesis cause alopecia with intellectual disability, a rare recessive neuroectodermal syndrome},
  author = {Thomas Besnard and Natacha Sloboda and Alice Goldenberg and Sébastien Küry and Benjamin Cogné and Flora Breheret and Eva Trochu and Solène Conrad and Marie Vincent and Wallid Deb and Xavier Balguerie and Sébastien Barbarot and Geneviève Baujat and Tawfeg Ben-Omran and Anne-Claire Bursztejn and Virginie Carmignac and Alexandre N. Datta and Aline Delignières and Laurence Faivre and Betty Gardie and Jean-Louis Guéant and Paul Kuentz and Marion Lenglet and Marie-Cécile Nassogne and Vincent Ramaekers and Rhonda E. Schnur and Yue Si and Erin Torti and Julien Thevenon and Pierre Vabres and Lionel Van Maldergem and Dorothea Wand and Arnaud Wiedemann and Bertrand Cariou and Richard Redon and Antonin Lamazière and Stéphane Bézieau and Francois Feillet and Bertrand Isidor},
  year = {2019},
  journal = {Genetics in Medicine},
  doi = {10.1038/s41436-019-0445-x},
  url = {https://doi.org/10.1038/s41436-019-0445-x}
}

RIS

TY  - JOUR
TI  - Biallelic pathogenic variants in the lanosterol synthase gene LSS involved in the cholesterol biosynthesis cause alopecia with intellectual disability, a rare recessive neuroectodermal syndrome
AU  - Thomas Besnard
AU  - Natacha Sloboda
AU  - Alice Goldenberg
AU  - Sébastien Küry
AU  - Benjamin Cogné
AU  - Flora Breheret
AU  - Eva Trochu
AU  - Solène Conrad
AU  - Marie Vincent
AU  - Wallid Deb
AU  - Xavier Balguerie
AU  - Sébastien Barbarot
AU  - Geneviève Baujat
AU  - Tawfeg Ben-Omran
AU  - Anne-Claire Bursztejn
AU  - Virginie Carmignac
AU  - Alexandre N. Datta
AU  - Aline Delignières
AU  - Laurence Faivre
AU  - Betty Gardie
AU  - Jean-Louis Guéant
AU  - Paul Kuentz
AU  - Marion Lenglet
AU  - Marie-Cécile Nassogne
AU  - Vincent Ramaekers
AU  - Rhonda E. Schnur
AU  - Yue Si
AU  - Erin Torti
AU  - Julien Thevenon
AU  - Pierre Vabres
AU  - Lionel Van Maldergem
AU  - Dorothea Wand
AU  - Arnaud Wiedemann
AU  - Bertrand Cariou
AU  - Richard Redon
AU  - Antonin Lamazière
AU  - Stéphane Bézieau
AU  - Francois Feillet
AU  - Bertrand Isidor
PY  - 2019
JO  - Genetics in Medicine
DO  - 10.1038/s41436-019-0445-x
UR  - https://doi.org/10.1038/s41436-019-0445-x
ER  - 

APA

Besnard, T., Sloboda, N., Goldenberg, A., Küry, S., Cogné, B., Breheret, F., Trochu, E., Conrad, S., Vincent, M., Deb, W., Balguerie, X., Barbarot, S., Baujat, G., Ben-Omran, T., Bursztejn, A., Carmignac, V., Datta, A. N., Delignières, A., Faivre, L., Gardie, B., Guéant, J., Kuentz, P., Lenglet, M., Nassogne, M., Ramaekers, V., Schnur, R. E., Si, Y., Torti, E., Thevenon, J., Vabres, P., Maldergem, L. V., Wand, D., Wiedemann, A., Cariou, B., Redon, R., Lamazière, A., Bézieau, S., Feillet, F., & Isidor, B. (2019). Biallelic pathogenic variants in the lanosterol synthase gene LSS involved in the cholesterol biosynthesis cause alopecia with intellectual disability, a rare recessive neuroectodermal syndrome. Genetics in Medicine. https://doi.org/10.1038/s41436-019-0445-x

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