LMNA R527C pathogenic variant causes an inflammation-driven segmental progeroid syndrome via triggering DNA-sensing pathways.

Zhao Y, Liu T, Shu W, Wang D, Wang H, Liu X, Jiao X, Li J, Liu T, Kuang M, Li R, Du H, Zhang Z, Zhou Z, Guo X, Wei X, Liu T, Li Y, Liu S, Chen J, Luo Y, Xia H, Cao L, Tian W, Sun X, Dong W, Zhou G, Gao X, Li Y, Liu S, Liu X, Lu D, Zhou Q, Zhao P, You F

Open source

DOI: 10.1093/procel/pwag061
Published: 2026 Aug 25
Container: Protein & cell
Publisher: Not recorded
Open access: unknown

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Cite this work

BibTeX

@article{allodium:10.1093/procel/pwag061,
  title = {LMNA R527C pathogenic variant causes an inflammation-driven segmental progeroid syndrome via triggering DNA-sensing pathways.},
  author = {Zhao Y and Liu T and Shu W and Wang D and Wang H and Liu X and Jiao X and Li J and Liu T and Kuang M and Li R and Du H and Zhang Z and Zhou Z and Guo X and Wei X and Liu T and Li Y and Liu S and Chen J and Luo Y and Xia H and Cao L and Tian W and Sun X and Dong W and Zhou G and Gao X and Li Y and Liu S and Liu X and Lu D and Zhou Q and Zhao P and You F},
  year = {2026},
  journal = {Protein \& cell},
  doi = {10.1093/procel/pwag061},
  url = {https://doi.org/10.1093/procel/pwag061}
}

RIS

TY  - JOUR
TI  - LMNA R527C pathogenic variant causes an inflammation-driven segmental progeroid syndrome via triggering DNA-sensing pathways.
AU  - Zhao Y
AU  - Liu T
AU  - Shu W
AU  - Wang D
AU  - Wang H
AU  - Liu X
AU  - Jiao X
AU  - Li J
AU  - Liu T
AU  - Kuang M
AU  - Li R
AU  - Du H
AU  - Zhang Z
AU  - Zhou Z
AU  - Guo X
AU  - Wei X
AU  - Liu T
AU  - Li Y
AU  - Liu S
AU  - Chen J
AU  - Luo Y
AU  - Xia H
AU  - Cao L
AU  - Tian W
AU  - Sun X
AU  - Dong W
AU  - Zhou G
AU  - Gao X
AU  - Li Y
AU  - Liu S
AU  - Liu X
AU  - Lu D
AU  - Zhou Q
AU  - Zhao P
AU  - You F
PY  - 2026
JO  - Protein & cell
DO  - 10.1093/procel/pwag061
UR  - https://doi.org/10.1093/procel/pwag061
ER  -

APA

Y, Z., T, L., W, S., D, W., H, W., X, L., X, J., J, L., T, L., M, K., R, L., H, D., Z, Z., Z, Z., X, G., X, W., T, L., Y, L., S, L., J, C., Y, L., H, X., L, C., W, T., X, S., W, D., G, Z., X, G., Y, L., S, L., X, L., D, L., Q, Z., P, Z., & F, Y. (2026). LMNA R527C pathogenic variant causes an inflammation-driven segmental progeroid syndrome via triggering DNA-sensing pathways.. Protein & cell. https://doi.org/10.1093/procel/pwag061

Source records

pubmed · retrieved 2026-09-25T01:22:03.690Z