In silico, in vitro and ex vivo characterization of cystic fibrosis transmembrane conductance regulator pathogenic variants localized in the fourth intracellular loop and their rescue by modulators.

Pesce E, Tomati V, Capurro V, Lena M, Pastorino C, Astore M, Kuyucak S, Chevalier B, Sondo E, Cresta F, Dighero A, Terlizzi V, Fevola C, Costa S, Lucanto MC, Daccò V, Claut L, Ficili F, Fabrizzi B, Bocciardi R, Zara F, Castellani C, Galietta LJV, Waters SA, Hinzpeter A, Pedemonte N

Open source

DOI: 10.1111/bph.70176
Published: 2025 Dec
Container: British journal of pharmacology
Publisher: Not recorded
Open access: unknown

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Cite this work

BibTeX

@article{allodium:10.1111/bph.70176,
  title = {In silico, in vitro and ex vivo characterization of cystic fibrosis transmembrane conductance regulator pathogenic variants localized in the fourth intracellular loop and their rescue by modulators.},
  author = {Pesce E and Tomati V and Capurro V and Lena M and Pastorino C and Astore M and Kuyucak S and Chevalier B and Sondo E and Cresta F and Dighero A and Terlizzi V and Fevola C and Costa S and Lucanto MC and Daccò V and Claut L and Ficili F and Fabrizzi B and Bocciardi R and Zara F and Castellani C and Galietta LJV and Waters SA and Hinzpeter A and Pedemonte N},
  year = {2025},
  journal = {British journal of pharmacology},
  doi = {10.1111/bph.70176},
  url = {https://doi.org/10.1111/bph.70176}
}

RIS

TY  - JOUR
TI  - In silico, in vitro and ex vivo characterization of cystic fibrosis transmembrane conductance regulator pathogenic variants localized in the fourth intracellular loop and their rescue by modulators.
AU  - Pesce E
AU  - Tomati V
AU  - Capurro V
AU  - Lena M
AU  - Pastorino C
AU  - Astore M
AU  - Kuyucak S
AU  - Chevalier B
AU  - Sondo E
AU  - Cresta F
AU  - Dighero A
AU  - Terlizzi V
AU  - Fevola C
AU  - Costa S
AU  - Lucanto MC
AU  - Daccò V
AU  - Claut L
AU  - Ficili F
AU  - Fabrizzi B
AU  - Bocciardi R
AU  - Zara F
AU  - Castellani C
AU  - Galietta LJV
AU  - Waters SA
AU  - Hinzpeter A
AU  - Pedemonte N
PY  - 2025
JO  - British journal of pharmacology
DO  - 10.1111/bph.70176
UR  - https://doi.org/10.1111/bph.70176
ER  -

APA

E, P., V, T., V, C., M, L., C, P., M, A., S, K., B, C., E, S., F, C., A, D., V, T., C, F., S, C., MC, L., V, D., L, C., F, F., B, F., R, B., F, Z., C, C., LJV, G., SA, W., A, H., & N, P. (2025). In silico, in vitro and ex vivo characterization of cystic fibrosis transmembrane conductance regulator pathogenic variants localized in the fourth intracellular loop and their rescue by modulators.. British journal of pharmacology. https://doi.org/10.1111/bph.70176

Source records

pubmed · retrieved 2026-09-27T01:08:56.924Z