Persistence of lung hyperinflation and small airway dysfunction in school-aged children with cystic fibrosis treated with elexacaftor-tezacaftor-ivacaftor: results from the real-world MODUL-CF study.

Colin L, Delaup V, Le Bourgeois M, Neve V, Wizla-Derambure N, Ioan IC, Tatopoulos A, Kieffer S, Blonde A, Bokov P, Houdoin V, Le Clainche L, Barzic A, Ohlmann C, Toin T, Perrin T, Coutier L, Abou Taam R, Bonnel AS, Rignani A, Feghali H, Bui S, Fayon M, Letierce A, Sermet-Gaudelus I, Reix P

Open source

DOI: 10.1183/23120541.01585-2025
Published: 2026 May
Container: ERJ open research
Publisher: Not recorded
Open access: yes

Credibility signals

uncertain Score 53/100 under policy 1.0.0. This is a metadata assessment, not a judgment of the paper's conclusions.

Show all credibility signals

cautionDOI registered: No matching Crossref record was present in this response. Source: Crossref; license: CC0 metadata
cautionDOI resolves: No matching Crossref record was present in this response. Source: Crossref; license: CC0 metadata
supportingDirectory of Open Access Journals: A matching record was returned by DOAJ. Source: DOAJ; license: CC0
not scoredMEDLINE indexed: Not checked or no result supplied; no credibility inference made. Source: No authority result supplied; license: Unknown
not scoredOpenAlex core source: Not checked or no result supplied; no credibility inference made. Source: No authority result supplied; license: Unknown
not scoredKnown publisher allow-list: Not checked or no result supplied; no credibility inference made. Source: No authority result supplied; license: Unknown
not scoredROR affiliation: Not checked or no result supplied; no credibility inference made. Source: No authority result supplied; license: Unknown
not scoredRetraction Watch retraction: No retraction notice matched this DOI in the deployed snapshot. No matching event found; coverage may be incomplete. Source: Retraction Watch; license: CC BY 4.0
not scoredRetraction Watch expression of concern: No expression of concern notice matched this DOI in the deployed snapshot. No matching event found; coverage may be incomplete. Source: Retraction Watch; license: CC BY 4.0
not scoredRetraction Watch correction: No correction notice matched this DOI in the deployed snapshot. No matching event found; coverage may be incomplete. Source: Retraction Watch; license: CC BY 4.0
not scoredRetraction Watch reinstatement: No reinstatement notice matched this DOI in the deployed snapshot. No matching event found; coverage may be incomplete. Source: Retraction Watch; license: CC BY 4.0
supportingOpen access status: Normalized open-access status: open. Source: Normalized work metadata; license: Caller-provided; provenance license not supplied to scorer
not scoredPublication license: Not checked or no result supplied; no credibility inference made. Source: No authority result supplied; license: Unknown
not scoredPublication version: A publication version was supplied but is not scored. Source: Normalized work metadata; license: Caller-provided; provenance license not supplied to scorer
cautionMetadata completeness: 5 of 6 scored descriptive metadata groups are present; missing fields increase uncertainty. Source: Normalized work metadata; license: Caller-provided; provenance license not supplied to scorer

Cite this work

BibTeX

@article{allodium:10.1183/23120541.01585-2025,
  title = {Persistence of lung hyperinflation and small airway dysfunction in school-aged children with cystic fibrosis treated with elexacaftor-tezacaftor-ivacaftor: results from the real-world MODUL-CF study.},
  author = {Colin L and Delaup V and Le Bourgeois M and Neve V and Wizla-Derambure N and Ioan IC and Tatopoulos A and Kieffer S and Blonde A and Bokov P and Houdoin V and Le Clainche L and Barzic A and Ohlmann C and Toin T and Perrin T and Coutier L and Abou Taam R and Bonnel AS and Rignani A and Feghali H and Bui S and Fayon M and Letierce A and Sermet-Gaudelus I and Reix P},
  year = {2026},
  journal = {ERJ open research},
  doi = {10.1183/23120541.01585-2025},
  url = {https://doi.org/10.1183/23120541.01585-2025}
}

RIS

TY  - JOUR
TI  - Persistence of lung hyperinflation and small airway dysfunction in school-aged children with cystic fibrosis treated with elexacaftor-tezacaftor-ivacaftor: results from the real-world MODUL-CF study.
AU  - Colin L
AU  - Delaup V
AU  - Le Bourgeois M
AU  - Neve V
AU  - Wizla-Derambure N
AU  - Ioan IC
AU  - Tatopoulos A
AU  - Kieffer S
AU  - Blonde A
AU  - Bokov P
AU  - Houdoin V
AU  - Le Clainche L
AU  - Barzic A
AU  - Ohlmann C
AU  - Toin T
AU  - Perrin T
AU  - Coutier L
AU  - Abou Taam R
AU  - Bonnel AS
AU  - Rignani A
AU  - Feghali H
AU  - Bui S
AU  - Fayon M
AU  - Letierce A
AU  - Sermet-Gaudelus I
AU  - Reix P
PY  - 2026
JO  - ERJ open research
DO  - 10.1183/23120541.01585-2025
UR  - https://doi.org/10.1183/23120541.01585-2025
ER  -

APA

L, C., V, D., M, L. B., V, N., N, W., IC, I., A, T., S, K., A, B., P, B., V, H., L, L. C., A, B., C, O., T, T., T, P., L, C., R, A. T., AS, B., A, R., H, F., S, B., M, F., A, L., I, S., & P, R. (2026). Persistence of lung hyperinflation and small airway dysfunction in school-aged children with cystic fibrosis treated with elexacaftor-tezacaftor-ivacaftor: results from the real-world MODUL-CF study.. ERJ open research. https://doi.org/10.1183/23120541.01585-2025

Source records

pubmed · retrieved 2026-09-27T00:37:10.706Z
europe-pmc · retrieved 2026-09-27T00:37:10.719Z
doaj · retrieved 2026-09-27T00:37:10.731Z