Recurrent fever and association with severe organ involvement, mortality and treatment outcomes in VEXAS syndrome: data from the AIDA Network

Valeria Caggiano, Jessica Sbalchiero, Micol Frassi, Francesca Crisafulli, Ilaria Cavazzana, Andrea Hinojosa-Azaola, Eduardo Martín-Nares, Guillermo Arturo Guaracha-Basañez, Jiram Torres-Ruiz, Ewa Wiesik-Szewczyk, Anna Nowakowska-Plaza, Paolo Sfriso, Sara Bindoli, Samuele Rizzo, José Hernández-Rodríguez, Verónica Gómez-Caverzaschi, Olga Araújo, Henrique A. Mayrink Giardini, Andrés González-García, Giuseppe Lopalco, Ombretta Viapiana, Riccardo Bixio, Abdurrahman Tufan, Pravin Hissaria, Mark Beecher, Alicia Callisto, Amato De Paulis, Lorenzo Dagna, Corrado Campochiaro, Alessandro Tomelleri, Serena Bugatti, Alessandra Milanesi, Guillermo Ruiz-Irastorza, Adriana Soto-Peleteiro, Matteo Piga, Alberto Cauli, Fabrizio Conti, Chiara Cardamone, Paola Triggianese, Carmelo Gurnari, Rosetta Vitetta, Marcella Prete, Vito Racanelli, Rosaria Talarico, Francesco Ferro, Federica di Cianni, Maria Chiara Cuccaro, Adrián Mayo-Juanatey, Alessandra Renieri, Vincenzo Sorrentino, Mehmet Ali Ergun, Alberto Balistreri, Bruno Frediani, Monica Bocchia, Claudia Fabiani, Luca Cantarini, Antonio Vitale

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DOI
10.3389/fimmu.2026.1753412
Published
2026-03-13
Container
Frontiers in Immunology
Publisher
Frontiers Media SA
Open access
unknown

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BibTeX

@article{allodium:10.3389/fimmu.2026.1753412,
  title = {Recurrent fever and association with severe organ involvement, mortality and treatment outcomes in VEXAS syndrome: data from the AIDA Network},
  author = {Valeria Caggiano and Jessica Sbalchiero and Micol Frassi and Francesca Crisafulli and Ilaria Cavazzana and Andrea Hinojosa-Azaola and Eduardo Martín-Nares and Guillermo Arturo Guaracha-Basañez and Jiram Torres-Ruiz and Ewa Wiesik-Szewczyk and Anna Nowakowska-Plaza and Paolo Sfriso and Sara Bindoli and Samuele Rizzo and José Hernández-Rodríguez and Verónica Gómez-Caverzaschi and Olga Araújo and Henrique A. Mayrink Giardini and Andrés González-García and Giuseppe Lopalco and Ombretta Viapiana and Riccardo Bixio and Abdurrahman Tufan and Pravin Hissaria and Mark Beecher and Alicia Callisto and Amato De Paulis and Lorenzo Dagna and Corrado Campochiaro and Alessandro Tomelleri and Serena Bugatti and Alessandra Milanesi and Guillermo Ruiz-Irastorza and Adriana Soto-Peleteiro and Matteo Piga and Alberto Cauli and Fabrizio Conti and Chiara Cardamone and Paola Triggianese and Carmelo Gurnari and Rosetta Vitetta and Marcella Prete and Vito Racanelli and Rosaria Talarico and Francesco Ferro and Federica di Cianni and Maria Chiara Cuccaro and Adrián Mayo-Juanatey and Alessandra Renieri and Vincenzo Sorrentino and Mehmet Ali Ergun and Alberto Balistreri and Bruno Frediani and Monica Bocchia and Claudia Fabiani and Luca Cantarini and Antonio Vitale},
  year = {2026},
  journal = {Frontiers in Immunology},
  doi = {10.3389/fimmu.2026.1753412},
  url = {https://doi.org/10.3389/fimmu.2026.1753412}
}

RIS

TY  - JOUR
TI  - Recurrent fever and association with severe organ involvement, mortality and treatment outcomes in VEXAS syndrome: data from the AIDA Network
AU  - Valeria Caggiano
AU  - Jessica Sbalchiero
AU  - Micol Frassi
AU  - Francesca Crisafulli
AU  - Ilaria Cavazzana
AU  - Andrea Hinojosa-Azaola
AU  - Eduardo Martín-Nares
AU  - Guillermo Arturo Guaracha-Basañez
AU  - Jiram Torres-Ruiz
AU  - Ewa Wiesik-Szewczyk
AU  - Anna Nowakowska-Plaza
AU  - Paolo Sfriso
AU  - Sara Bindoli
AU  - Samuele Rizzo
AU  - José Hernández-Rodríguez
AU  - Verónica Gómez-Caverzaschi
AU  - Olga Araújo
AU  - Henrique A. Mayrink Giardini
AU  - Andrés González-García
AU  - Giuseppe Lopalco
AU  - Ombretta Viapiana
AU  - Riccardo Bixio
AU  - Abdurrahman Tufan
AU  - Pravin Hissaria
AU  - Mark Beecher
AU  - Alicia Callisto
AU  - Amato De Paulis
AU  - Lorenzo Dagna
AU  - Corrado Campochiaro
AU  - Alessandro Tomelleri
AU  - Serena Bugatti
AU  - Alessandra Milanesi
AU  - Guillermo Ruiz-Irastorza
AU  - Adriana Soto-Peleteiro
AU  - Matteo Piga
AU  - Alberto Cauli
AU  - Fabrizio Conti
AU  - Chiara Cardamone
AU  - Paola Triggianese
AU  - Carmelo Gurnari
AU  - Rosetta Vitetta
AU  - Marcella Prete
AU  - Vito Racanelli
AU  - Rosaria Talarico
AU  - Francesco Ferro
AU  - Federica di Cianni
AU  - Maria Chiara Cuccaro
AU  - Adrián Mayo-Juanatey
AU  - Alessandra Renieri
AU  - Vincenzo Sorrentino
AU  - Mehmet Ali Ergun
AU  - Alberto Balistreri
AU  - Bruno Frediani
AU  - Monica Bocchia
AU  - Claudia Fabiani
AU  - Luca Cantarini
AU  - Antonio Vitale
PY  - 2026
JO  - Frontiers in Immunology
DO  - 10.3389/fimmu.2026.1753412
UR  - https://doi.org/10.3389/fimmu.2026.1753412
ER  - 

APA

Caggiano, V., Sbalchiero, J., Frassi, M., Crisafulli, F., Cavazzana, I., Hinojosa-Azaola, A., Martín-Nares, E., Guaracha-Basañez, G. A., Torres-Ruiz, J., Wiesik-Szewczyk, E., Nowakowska-Plaza, A., Sfriso, P., Bindoli, S., Rizzo, S., Hernández-Rodríguez, J., Gómez-Caverzaschi, V., Araújo, O., Giardini, H. A. M., González-García, A., Lopalco, G., Viapiana, O., Bixio, R., Tufan, A., Hissaria, P., Beecher, M., Callisto, A., Paulis, A. D., Dagna, L., Campochiaro, C., Tomelleri, A., Bugatti, S., Milanesi, A., Ruiz-Irastorza, G., Soto-Peleteiro, A., Piga, M., Cauli, A., Conti, F., Cardamone, C., Triggianese, P., Gurnari, C., Vitetta, R., Prete, M., Racanelli, V., Talarico, R., Ferro, F., Cianni, F. D., Cuccaro, M. C., Mayo-Juanatey, A., Renieri, A., Sorrentino, V., Ergun, M. A., Balistreri, A., Frediani, B., Bocchia, M., Fabiani, C., Cantarini, L., & Vitale, A. (2026). Recurrent fever and association with severe organ involvement, mortality and treatment outcomes in VEXAS syndrome: data from the AIDA Network. Frontiers in Immunology. https://doi.org/10.3389/fimmu.2026.1753412

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