Characterization of the frameshift c.515dupC knock-in mouse model of HSPB8-associated myopathy (MFM13) and evaluation of Trehalose as autophagy-modulating therapy.

Shmara A, Weiss L, Gromova A, Tedesco B, Pal P, Kostalnick G, Boock V, Bassett E, Parera S, Cheng C, Ta L, Lee J, Panchagatti A, Mohanty E, Vu J, La Spada AR, Poletti A, Kimonis V

Open source

DOI
10.64898/2026.08.04.742148
Published
2026 Aug 9
Container
bioRxiv : the preprint server for biology
Publisher
Not recorded
Open access
yes

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BibTeX

@article{allodium:10.64898/2026.08.04.742148,
  title = {Characterization of the frameshift c.515dupC knock-in mouse model of HSPB8-associated myopathy (MFM13) and evaluation of Trehalose as autophagy-modulating therapy.},
  author = {Shmara A and Weiss L and Gromova A and Tedesco B and Pal P and Kostalnick G and Boock V and Bassett E and Parera S and Cheng C and Ta L and Lee J and Panchagatti A and Mohanty E and Vu J and La Spada AR and Poletti A and Kimonis V},
  year = {2026},
  journal = {bioRxiv : the preprint server for biology},
  doi = {10.64898/2026.08.04.742148},
  url = {https://doi.org/10.64898/2026.08.04.742148}
}

RIS

TY  - JOUR
TI  - Characterization of the frameshift c.515dupC knock-in mouse model of HSPB8-associated myopathy (MFM13) and evaluation of Trehalose as autophagy-modulating therapy.
AU  - Shmara A
AU  - Weiss L
AU  - Gromova A
AU  - Tedesco B
AU  - Pal P
AU  - Kostalnick G
AU  - Boock V
AU  - Bassett E
AU  - Parera S
AU  - Cheng C
AU  - Ta L
AU  - Lee J
AU  - Panchagatti A
AU  - Mohanty E
AU  - Vu J
AU  - La Spada AR
AU  - Poletti A
AU  - Kimonis V
PY  - 2026
JO  - bioRxiv : the preprint server for biology
DO  - 10.64898/2026.08.04.742148
UR  - https://doi.org/10.64898/2026.08.04.742148
ER  - 

APA

A, S., L, W., A, G., B, T., P, P., G, K., V, B., E, B., S, P., C, C., L, T., J, L., A, P., E, M., J, V., AR, L. S., A, P., & V, K. (2026). Characterization of the frameshift c.515dupC knock-in mouse model of HSPB8-associated myopathy (MFM13) and evaluation of Trehalose as autophagy-modulating therapy.. bioRxiv : the preprint server for biology. https://doi.org/10.64898/2026.08.04.742148

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